巨型肝血管平滑肌脂肪瘤伴包膜下破裂误诊为肝细胞癌1例报告

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摘要：肝血管平滑肌脂肪瘤（HAML）是一种罕见的良性间充质肿瘤，多发于中年女性，由于早期无明显症状，且缺乏特异的影像学表现，因此，诊断难度大，误诊率高。本文报道1例巨型HAML伴包膜下破裂误诊为肝细胞癌的病例，介绍其病例特点和诊治经过，期望为此类疾病的诊治提供参考。

关键词：肝肿瘤；血管肌脂瘤；误诊

基金项目：山西医科大学第一医院博士基金项目（SYYYRC-2023016）

Rare giant hepatic angiomyolipoma with subcapsular rupture misdiagnosed as hepatocellular carcinoma：A case report

ZHANG Zhiwei 1 ，LIU Feng 2 ，ZHANG Hezhao 3，4a ，WANG Qinying 4b ，SHI Zhiyong 3，4a

1. The First Clinical Medical College of Shanxi Medical University，Taiyuan 030000，China；2. Department of Head and Neck Surgery，Shanxi Cancer Hospital，Shanxi Hospital Affiliated to Cancer Hospital，Chinese Academy of Medical Sciences，Cancer Hospital Affiliated to Shanxi Medical University，Taiyuan 030000，China；3. Institute of Liver Disease，Shanxi Medical University，Taiyuan 030000，China；4. a. Department of Hepatobiliary Surgery，b. Department of Infectious Diseases，The First Hospital of Shanxi Medical University，Taiyuan 030000，China

Corresponding author：SHI Zhiyong，shizhiyong2015@163.com （ORCID：0000-0001-8379-9847）

Abstract：Hepatic angiomyolipoma （HAML） is a rare benign mesenchymal tumor frequently observed in middle-aged women. Due to the absence of prominent symptoms in the early stage and the lack of specific imaging findings，the diagnosis of this disease can be challenging，leading to a high rate of misdiagnosis. This article reports a case of giant HAML with subcapsular rupture that was misdiagnosed as hepatocellular carcinoma and introduces the characteristics of the case and its diagnosis and treatment process，in order to provide a reference for the diagnosis and treatment of this type of disease.

Key words：Liver Neoplasms；Angiomyolipomas；Diagnostic Errors

Research funding：The First Hospital of Shanxi Medical University Doctoral Fund Project （SYYYRC-2023016）

肝 血 管 平 滑 肌 脂 肪 瘤（hepatic angiomyolipoma，HAML）是一种罕见的良性间充质肿瘤，通常由血管、平滑肌细胞和成熟脂肪组织按不同比例组成［1］。（剩余12613字）